Complete Thoracic Ectopia Cordis, Dilemma of the Outcome: A Case Report
نویسندگان
چکیده
Background: Ectopia Cordis (EC) is a rare congenital condition where the heart partially or completely lies outside thoracic cavity (extrathoracic), uncovered by pericardium and skin. Many works of literature reported EC abnormality with an incidence about 5-8 per 1 million live births includes 0.1% diseases. Methods: This was male baby, weighing 2.900 kg, received cyanosis defect in anterior chest wall protruding out through it. On initial physical examination, split sternum complete (beating absence apex pointing upwards) were reported. Results: The baby’s poor general did not allow further radiologic studies echocardiography could be performed. By time, arrangement had been planned for him to undergo cardiothoracic referral; unfortunately, he ran downhill course succumbed within 36 hours life. Conclusion: important submitting such findings will assist our team: pediatric surgeons, obstetricians, pediatricians and, neonatal intensivists develop future management strategies when they are enrolled confronted cases, improving outcome precise workup design provide optimal evaluation, diagnosis, roadmaps potential cases EC.
منابع مشابه
Partial Ectopia Cordis: A Case Report
Background: One-third of all major congenital anomalies are Congenital heart disease (CHD) and Reported CHD prevalence increased over time and in Asian countries is more than western countries. Ectopia cordis (EC) is a rare congenital anomaly with an estimated incidence of 1:100 000 live births in developed countries. EC is characterized by abnormal heart placement outside the thorax, mostly on...
متن کاملComplete Ectopia Cordis: A Case Report and Literature Review
Ectopia cordis is a congenital heart exposure defined as complete or partial protrusion of heart through ventral defect in the thoracoabdominal wall alone or with other viscera in cases of pentalogy of Cantrell. This condition was first described by Haller et al. in 1706; since then many advances have been made. Diagnosis of ectopia cordis is done prenatally in well-equipped health facility by ...
متن کاملEctopia Cordis anesthetic considerations a case report
Introduction: Ectopia cordis is a rare congenital defect and a true neonatal surgical emergency, with an occurrence of 5.5 to 7.9 cases per million live births [1]. This impressive malformation develops due to failure of maturation of the midline mesodermal components of the chest and abdomen [2]. The disorder is classified into five anatomical types including cervical, cervicothoracic, thoraci...
متن کاملA Rare Case Report of Thoracic Ectopia Cordis: An Obstetrician's Point of View in Multidisciplinary Approach
Ectopia cordis is a rare congenital anomaly associated with the heart positioned outside of the thoracic cavity either partially or completely. It can be associated with other congenital abnormalities. Overall, the prognosis for infants with ectopia cordis is very poor but depends greatly on the type and severity of ectopia cordis and intracardiac and associated malformations. We present one ca...
متن کاملThoracic Ectopia Cordis in an Ethiopian Neonate
BACKGROUND Ectopia Cordis is defined as complete or partial displacement of the heart outside the thoracic cavity. It is a rare congenital defect with failure of fusion of the sternum with extra thoracic location of the heart. The estimated prevalence of this case is 5.5 to 7.9 per million live births. CASE PRESENTATION We had a case of a 16-hour-old male neonate weighing 2.9kg with externall...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Surgical Case Reports
سال: 2021
ISSN: ['2198-7793']
DOI: https://doi.org/10.31487/j.scr.2021.04.05